posted on 2020-07-01, 08:44authored byMiyawaki E.K., Hsu L., Bhattacharyya S., O’Hare M.J., Roy A., Kett L., Caplan R.A., Dattilo L.W., Jo V.Y., Guenette J.P.
We report two cases of biopsy-corroborated “fibrosing inflammatory pseudotumor” to illustrate that the entity, rarely described in the neurological literature, should be included in the differential diagnosis of either a cranial mononeuropathy or, certainly, in the case of progressive cranial neuropathies. A broad differential diagnosis arises in certain contexts. Early steroid treatment can be effective, and perhaps later-generation immune-modulating agents may confer further options, although there is no known definitive treatment.