posted on 2024-07-03, 12:38authored byBenedettiPedroza J., CarrascoGarcía I., MartínezBernal G., MirasRodriguez I.
Inflammatory myofibroblastic tumor is a rare entity, classified within soft tissue sarcomas. It is an intermediate malignancy tumor, which seldom presents as metastatic disease. The treatment of choice is surgery, except in cases where surgery is not possible due to localization or if it presents with metastatic disease. Approximately 50% of IMTs will exhibit ALK translocation, providing a therapeutic target for these patients.
A case is presented of a patient with metastatic IMT in complete response to treatment with alectinib, maintained for over 4 years.